Okla. Stat. tit. 63, § 63-5026: Medicaid prescription drug program – Definition of

phenylketonuria.

A. The Oklahoma Health Care Authority Board shall, in

administering the Medicaid prescription drug program, utilize the

following definition for "phenylketonuria" to mean: An inborn error

of metabolism attributable to a deficiency of or a defect in

phenylalanine hydroxylase, the enzyme that catalyzes the conversion

of phenylalanine to tyrosine. The deficiency permits the

accumulation of phenylalanine and its metabolic products in the body

fluids. The deficiency can result in intellectual disabilities

(phenylpyruvic oligophrenia), neurologic manifestations (including

hyperkinesia, epilepsy, and microcephaly), light pigmentation, and

eczema. The disorder is transmitted as an autosomal recessive trait

and can be treated by administration of a diet low in phenylalanine.

B. The Oklahoma Health Care Authority Board shall promulgate

any rules necessary to effectuate the provisions of this section.